A 14-year-old in heart failure with multiple cardiomyopathy variants illustrates a role for signal-to-noise analysis in gene test re-interpretation.

Abstract

Variants of unknown significance in cardiomyopathic disease should be analyzed systematically based on the prevalence of the variant in the population compared to prevalence of disease, evidence that other variants in the gene are pathologic, consistency of prediction software on pathogenicity, and the current clinical consensus.

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Citation

Published Version (Please cite this version)

10.1002/ccr3.1920

Publication Info

Connell, Patrick S, Aamir Jeewa, Debra L Kearney, Hari Tunuguntla, Susan W Denfield, Hugh D Allen and Andrew P Landstrom (2019). A 14-year-old in heart failure with multiple cardiomyopathy variants illustrates a role for signal-to-noise analysis in gene test re-interpretation. Clinical case reports, 7(1). pp. 211–217. 10.1002/ccr3.1920 Retrieved from https://hdl.handle.net/10161/20302.

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