Anomalous Origin of the Right Coronary Artery from the Pulmonary Artery in a Neonate with Turner Syndrome and Aortic Arch Hypoplasia.

Stefek, Bryan P

Imundo, Jason R

Clark, Joseph B

2023-12-04T15:33:13Z

2023-12-04T15:33:13Z

2019-06

2023-12-04T15:33:11Z

Anomalous origin of the right coronary artery from the pulmonary artery, a rare congenital cardiac defect, is typically not diagnosed during infancy. On the other hand, Turner syndrome is usually diagnosed early, and it is classically associated with bicuspid aortic valve and aortic coarctation. Individuals with Turner syndrome are also at increased risk for coronary artery anomalies. We present a case of anomalous right coronary artery from the pulmonary artery in a week-old neonate who also had Turner syndrome, patent ductus arteriosus, transverse aortic arch hypoplasia, and impaired ventricular function. Prostaglandin therapy through the ductus increased the patient's myocardial perfusion. Four months after corrective surgery, she was doing well. We discuss the reperfusion phenomenon in our patient's case, as well as other considerations in this combination of congenital defects.

0730-2347

1526-6702

https://hdl.handle.net/10161/29462

eng

Texas Heart Institute Journal

Texas Heart Institute journal

10.14503/thij-17-6521

Aorta, Thoracic

Coronary Vessels

Pulmonary Artery

Humans

Turner Syndrome

Coronary Vessel Anomalies

Abnormalities, Multiple

Fluoroscopy

Echocardiography

Blood Vessel Prosthesis Implantation

Infant, Newborn

Female

Cardiac Catheterization

Computed Tomography Angiography

Anomalous Origin of the Right Coronary Artery from the Pulmonary Artery in a Neonate with Turner Syndrome and Aortic Arch Hypoplasia.

Journal article

225

228

3

Duke

School of Medicine

Clinical Science Departments

Surgery

Surgery, Cardiovascular and Thoracic Surgery

Published

46